Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. HS being a hemolytic defect, frequently increased iron overload was not unexpected. Journal of Medical Cases.

Clinico-hematological profile of hereditary spherocytosis: Thrombo-embolic disease after splenectomy for hereditary stomatocytosis. Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. Am J Hematol ;57 1: Polish Academjy of Sciences? ahemia

Guidelines for the diagnosis and management of hereditary spherocytosis update. Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established.


Erythroid membrane protein defects in hereditary spherocytosis. Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: Splenectomy for hereditary spherocytosis: Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements.

The Efserocitosis survey on hereditary spherocytosis. Thus it becomes possible to screen for both hereditary and secondary spherocytosis.

Anemia Esferocitosis Hereditaria by Danna flores cuadros on Prezi

Este hecho explica la discrepancia entre estos valores. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis.

Monitoring of blood glucose and ferritin is recommended. The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the latter, as it is also seen in genetic hemochromatosis.

Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms. King on behalf of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis.


Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria.

Blood Cells Mol Dis ; J Lab Clin Med. This explains the discrepancy between these values.

Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis. Bienvenido a siicsalud Contacto Inquietudes.

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Se recomienda el monitoreo de glucemia y ferritina. Revista Cubana Hematol Inmunol Hemoter ;18 1: Referencias -Mayelin Herrera Garcia. Servicio de ayuda de la revista. A study of 62 Spanish cases. Br J Haematol ;93 2: Int J Pediatr Hematol Oncol ; 2: J Thromb Thrombolysis ;17 3: Oxygen affinity and compensated hemolysis in hereditary spherocytosis. Aires, Argentina; 16 2: